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Management of Difficult Airway With Laryngeal Mask in a Child With Mucopolysaccharidosis and Mitral Regurgitation: A Case Report

Mohsen Ziyaeifard 1 , Rasoul Azarfarin 1 , * , Rasoul Ferasatkish 1 and Majid Dashti 1
Authors Information
1 Rajaie Cardiovascular Medical and Research Center, Iran University of Medical Sciences, Tehran, IR Iran
Article information
  • Research in Cardiovascular Medicine: May 2014, 3 (2); e17456
  • Published Online: April 1, 2014
  • Article Type: Case Report
  • Received: January 7, 2014
  • Revised: March 9, 2014
  • Accepted: March 10, 2014
  • DOI: 10.5812/cardiovascmed.17456

To Cite: Ziyaeifard M, Azarfarin R, Ferasatkish R, Dashti M. Management of Difficult Airway With Laryngeal Mask in a Child With Mucopolysaccharidosis and Mitral Regurgitation: A Case Report, Res Cardiovasc Med. 2014 ;3(2):e17456. doi: 10.5812/cardiovascmed.17456.

Copyright: Copyright © 2014, Research in Cardiovascular Medicine. .
1. Introduction
2. Case Presentation
3. Discussion
  • 1. Cattano D, Killoran PV, Iannucci D, Maddukuri V, Altamirano AV, Sridhar S, et al. Anticipation of the difficult airway: preoperative airway assessment, an educational and quality improvement tool. Br J Anaesth. 2013; 111(2): 276-85[DOI][PubMed]
  • 2. Rodrigues AJ, Scordamaglio PR, Palomino AM, de Oliveira EQ, Jacomelli M, Figueiredo VR. Difficult airway intubation with flexible bronchoscope. Rev Bras Anestesiol. 2013; 63(4): 358-61[DOI][PubMed]
  • 3. Walker R, Belani KG, Braunlin EA, Bruce IA, Hack H, Harmatz PR, et al. Anaesthesia and airway management in mucopolysaccharidosis. J Inherit Metab Dis. 2013; 36(2): 211-9[DOI][PubMed]
  • 4. Valayannopoulos V, Nicely H, Harmatz P, Turbeville S. Mucopolysaccharidosis VI. Orphanet J Rare Dis. 2010; 5: 5[DOI][PubMed]
  • 5. Sayilgan C, Yuceyar L, Akbas S, Erolcay H. Anesthesia in a child with Maroteaux-Lamy syndrome undergoing mitral valve replacement. Clinics (Sao Paulo). 2012; 67(6): 693-6[PubMed]
  • 6. Kamin W. Diagnosis and management of respiratory involvement in Hunter syndrome. Acta Paediatr Suppl. 2008; 97(457): 57-60[DOI][PubMed]
  • 7. Chan YL, Lin SP, Man TT, Cheng CR. Clinical experience in anesthetic management for children with mucopolysaccharidoses: Report of ten cases. Acta Paediatr Taiwan. 2001; 42(5): 306-8[PubMed]
  • 8. Suh SH, Okutani R, Nakasuji M, Nakata K. Anesthesia in a patient with mucopolysaccharidosis type VI (Maroteaux-Lamy syndrome). J Anesth. 2010; 24(6): 945-8[DOI][PubMed]
  • 9. Herrick IA, Rhine EJ. The mucopolysaccharidoses and anaesthesia: a report of clinical experience. Can J Anaesth. 1988; 35(1): 67-73[DOI][PubMed]
  • 10. Muhlebach MS, Wooten W, Muenzer J. Respiratory manifestations in mucopolysaccharidoses. Paediatr Respir Rev. 2011; 12(2): 133-8[DOI][PubMed]
  • 11. Wold SM, Derkay CS, Darrow DH, Proud V. Role of the pediatric otolaryngologist in diagnosis and management of children with mucopolysaccharidoses. Int J Pediatr Otorhinolaryngol. 2010; 74(1): 27-31[DOI][PubMed]
  • 12. Wippermann CF, Beck M, Schranz D, Huth R, Michel-Behnke I, Jungst BK. Mitral and aortic regurgitation in 84 patients with mucopolysaccharidoses. Eur J Pediatr. 1995; 154(2): 98-101[PubMed]
  • 13. John A, Fagondes S, Schwartz I, Azevedo AC, Barrios P, Dalcin P, et al. Sleep abnormalities in untreated patients with mucopolysaccharidosis type VI. Am J Med Genet A. 2011; 155A(7): 1546-51[DOI][PubMed]
  • 14. Taguchi S, Kusunoki S, Fukuda H, Hamada H, Kawamoto M. [Difficult tracheal intubation using airway scope in a pediatric patient with Hunter syndrome]. Masui. 2009; 58(10): 1278-81[PubMed]
  • 15. Golzari SE, Khan ZH, Ghabili K, Hosseinzadeh H, Soleimanpour H, Azarfarin R, et al. Contributions of Medieval Islamic physicians to the history of tracheostomy. Anesth Analg. 2013; 116(5): 1123-32[DOI][PubMed]
  • 16. Soleimanpour H, Gholipouri C, Panahi JR, Afhami MR, Ghafouri RR, Golzari SE, et al. Role of anesthesiology curriculum in improving bag-mask ventilation and intubation success rates of emergency medicine residents: a prospective descriptive study. BMC Emerg Med. 2011; 11: 8[DOI][PubMed]
  • 17. Ziyaeifard M, Azarfarin R, Massoumi G. A comparison of intraocular pressure and hemodynamic responses to insertion of laryngeal mask airway or endotracheal tube using anesthesia with propofol and remifentanil in cataract surgery. J Res Med Sci. 2012; 17(6): 503-7[PubMed]
  • 18. Mofateh M, Ziaei fard M, Makhmalbaf G, nabei M. A case report of Post-Varicella Epiglottitis. J Birjand Univ Med Sci. 2008; 15(1)
  • 19. Azarfarin R, Seyedhejazi M, Golzari SE, Bilehjani E, Ghabili K, Alizadehasl A. Do pediatric patients undergoing cardiac surgeries require larger-size cuffed endotracheal tubes? A prospective study. Paediatr Anaesth. 2013; 23(3): 228-32[DOI][PubMed]
  • 20. Walker PP, Rose E, Williams JG. Upper airways abnormalities and tracheal problems in Morquio's disease. Thorax. 2003; 58(5): 458-9[PubMed]
  • 21. Braunlin EA, Harmatz PR, Scarpa M, Furlanetto B, Kampmann C, Loehr JP, et al. Cardiac disease in patients with mucopolysaccharidosis: presentation, diagnosis and management. J Inherit Metab Dis. 2011; 34(6): 1183-97[DOI][PubMed]
  • 22. Sugiyama T, Okutani R. Difficult tracheal intubation in a child with Cornelia de Lange syndrome using a paediatric Intlock installed in a Pentax Airway Scope. Anaesthesia. 2012; 67(12): 1411-2[DOI][PubMed]
  • 23. Torres MD, Calvo E, Fernandez Espla F, Gilsanz F. Anesthetic management of an adult patient with Cornelia de Lange Syndrome. Minerva Anestesiol. 2010; 76(3): 229-31[PubMed]
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